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Anti-GALNS Polyclonal Antibody
Cat: K004010P
Summary:
【Product name】:Anti-GALNS Polyclonal Antibody 【Source】:Rabbit
【Isotype】:IgG
【Gene ID】:2588 【Swiss Prot】:P34059
【Species reactivity】:Rat,Mouse,Human
【Tested applications】:IF,WB
【Immunogen】:Recombinant protein of human GALNS
【Storage】:Store at -20℃, avoid freeze/thaw cycles.
Background:
This gene encodes N-acetylgalactosamine-6-sulfatase which is a lysosomal exohydrolase required for the degradation of the glycosaminoglycans, keratan sulfate, and chondroitin 6-sulfate. Sequence alterations including point, missense and nonsense mutations, as well as those that affect splicing, result in a deficiency of this enzyme. Deficiencies of this enzyme lead to Morquio A syndrome, a lysosomal storage disorder.
Verified picture:
Immunohistochemistry of paraffin-embedded liver cancer(hu) using GALNS antibody at dilution of 1:100 (x100 lens,x200 lens).
Western blot analysis with GALNS antibody diluted at 1:1000;Lane: MCF7 HT-29 293T Mouse kidney Mouse brain Mouse intestine.
Immunofluorescence analysis of C6 cells using GALNS antibody diluted at 1:100.