Anti-ACADS Polyclonal Antibody
Cat: K008274P
Summary:
| 【Product name】：Anti-ACADS Polyclonal Antibody | 【Source】：Rabbit |
| 【Isotype】：IgG | |
| 【Gene ID】：35 | 【Swiss Prot】：P16219 |
| 【Species reactivity】：Human,Rat,Mouse | |
| 【Tested applications】：IHC,WB | |
| 【Immunogen】：Recombinant protein of human ACADS | |
| 【Storage】：Store at -20℃, avoid freeze/thaw cycles. | |
Background:
This gene encodes a a tetrameric mitochondrial flavoprotein, which is a member of the acyl-CoA dehydrogenase family. This enzyme catalyzes the initial step of the mitochondrial fatty acid beta-oxidation pathway. Mutations in this gene have been associated with Short Chain Acyl-CoA Dehydrogenase Deficiency. It is an autosomal recessive disorder resulting in acute acidosis and muscle weakness in infants, and a form of lipid-storage myopathy in adults.
Verified picture:
Western blot analysis with ACADS antibody diluted at 1:400; Lane:Mouse liver, Rat liver
Immunohistochemistry of paraffin-embedded Human colorectal cancer with ACADS antibody diluted at 1:50