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Anti-OTC Polyclonal Antibody - Cy3.5
Cat: K107189P - Cy3.5
Summary:
【Product name】:Anti-OTC Polyclonal Antibody - Cy3.5 【Source】:Rabbit
【Isotype】:IgG 【Purification】:Affinity purification
【Gene ID】:5009 【Swiss Prot】:P00480
【Tested applications】:IHC,WB
【Recommended dilution】:WB 1:5000-8000. IHC 1:100-300.
【Immunogen】:A synthetic peptide of human OTC
【Public Immunogen Range】:270-320/354aa
【Storage】:Store at -20℃. Avoid freeze/thaw cycles.
Background:
This nuclear gene encodes a mitochondrial matrix enzyme. Missense, nonsense, and frameshift mutations in this enzyme lead to ornithine transcarbamylase deficiency, which causes hyperammonemia. Since the gene for this enzyme maps close to that for Duchenne muscular dystrophy, it may play a role in that disease also.
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