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Anti-FKRP Polyclonal Antibody - SAlexa Fluor 660
Cat: K108717P - SAlexa Fluor 660
Summary:
【Product name】:Anti-FKRP Polyclonal Antibody - SAlexa Fluor 660 【Source】:Rabbit
【Isotype】:IgG
【Gene ID】:79147 【Swiss Prot】:Q9H9S5
【Species reactivity】:Human,Rat,Mouse
【Tested applications】:IHC
【Immunogen】:A synthetic peptide of Human FKRP
【Storage】:Store at -20℃, avoid freeze/thaw cycles.
Background:
Catalyzes the transfer of CDP-ribitol to ribitol 5-phosphate previously attached by FKTN/fukutin of to the phosphorylated O-mannosyl trisaccharide (N-acetylgalactosamine-beta-3-N-acetylglucosamine-beta-4-(phosphate-6-)mannose), a carbohydrate structure present in alpha-dystroglycan (DAG1). This constitutes the second step in the formation of the ribose 5-phosphate tandem repeat which links the phosphorylated O-mannosyl trisaccharide to the ligand binding moiety composed of repeats of 3-xylosyl-alpha-1,3-glucuronic acid-beta-1.
Verified picture: